去分化软骨肉瘤(dedifferentiated chondrosarcoma,DDCS)是一种较为罕见的原发性骨恶性肿瘤。去分化软骨肉瘤发病部位以股骨、胫骨最为多见,其次是骨盆,指(趾)骨少见,发生在肋骨者较少见报道。现报道杭州师范大学附属医院2010年7月收治的1例胸腔内肋骨起源的去分化软骨肉瘤的诊治经过,以提高临床医生对该病的认识。 Dedifferentiated chondrosarcoma (DDCS) is a rare primary malignancy of the bone. Differentiated chondrosarcoma to the incidence of parts of the femur, tibia most common, followed by the pelvis, finger (toe) bone rare, occurred in the ribs are less commonly reported. Is reported in Hangzhou Normal University Affiliated Hospital in July 2010 admitted to a case of rib rib sarcoma origin of dedifferentiated chondrosarcoma diagnosis and treatment to improve clinicians awareness of the disease.