真性肝脏畸胎瘤非常少见,文献报告仅23例,尚包括7个成人病例在内.本文报告1例小儿真性肝脏畸胎瘤,有高甲胎蛋白存在.目前24例肝脏畸胎瘤中,7例成人,17例小儿,多数年龄在3岁以下,女孩多见,其中11例有恶变,13例属良性.据本文作者Takuii Todani等收集的病例,特别发现在肝脏畸胎瘤患者,切除的肿瘤标本检查,肝脏组织比较常见,90%以上的病例有肝细胞 True liver teratoma is very rare, the literature reported only 23 cases, yet including seven adult cases, this article reports 1 case of pediatric true liver teratoma, a high presence of a-fetoprotein present 24 cases of liver teratoma, 7 adults, 17 children, most of the age of 3 years of age, more common in girls, 11 cases of malignant, 13 cases are benign.According to the author Takuii Todani and other cases collected, in particular, found in patients with teratoma liver, resection Tumor specimens, liver tissue is more common, more than 90% of cases have hepatocytes