原发性心脏恶性纤维组织细胞瘤极为罕见,占原发性心脏肿瘤的2%～3%[1]。国外自1978年至今陆续报道35例,国内至今仅发现3例[2,3,4]。由于缺乏足够的临床资料,对于该疾病的诊断、治疗等尚未有统一认识。我们报道1例并复习国内外共39例资料。个例　患者,女,36岁。因进行性气... Primary cardiac malignant fibrous histiocytoma is extremely rare, accounting for 2% to 3% of primary cardiac tumors [1]. 35 cases have been reported abroad since 1978, and only 3 cases have been found in China so far [2, 3, 4]. Due to the lack of adequate clinical data, there is no unified understanding of the diagnosis and treatment of the disease. We reported 1 case and reviewed 39 cases at home and abroad. A patient, female, 36 years old. Due to progressive gas ...