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目的探讨局灶皮层发育不良的临床病理学分型及特点。方法收集160例病理诊断为局灶皮层发育不良的难治性癫痫手术治疗患者的病理标本及临床资料。采用HE和免疫组织化学染色,探讨各种类型癫痫病理的临床病理学特点。结果局灶皮层发育不良160例,其中FCDⅠB134例、FCDⅡA16例、FCDⅡB10例。结论局灶皮层发育不良为引发难治性癫痫最常见病因,而亚型中以FCDⅠB型最为多见。免疫组化有助于FCD的诊断与分型。
Objective To investigate the clinicopathological types and features of focal cortical dysplasia. Methods The pathological specimens and clinical data of 160 patients with refractory epilepsy treated by pathological diagnosis of focal cortical dysplasia were collected. HE and immunohistochemical staining, to explore the clinical and pathological features of various types of epilepsy. Results 160 cases of focal cortical dysplasia, including FCD Ⅰ B134 cases, FCD Ⅱ A16 cases, FCD Ⅱ B10 cases. Conclusion Focal cortical dysplasia is the most common cause of refractory epilepsy, while FCD Ⅰ B is the most common in subtypes. Immunohistochemistry contributes to the diagnosis and classification of FCD.