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作者对家族遗传性淀粉样变病 AFp 型做了系统研究,以探讨其心脏病变类型和发病率。共327例病人,心电图异常者占87.2%(285人)。低电压和 V_1、V_2、V_3QS 波型分别为51.3%和35.7%。传导系统功能紊乱占64.5%(211例)。窦房结病,Ⅰ°与 Wencke-bach 室间传导阻滞常见。完全性房室传导阻
The authors made a systematic study of familial hereditary amyloidosis AFp type to investigate its type and incidence of heart disease. A total of 327 patients, 87.2% of patients with abnormal ECG (285). The low voltage and V_1, V_2 and V_3QS waveforms were 51.3% and 35.7% respectively. Conductive system dysfunction accounted for 64.5% (211 cases). Sinus node disease, I ° and Wencke-bach interventricular block common. Complete atrioventricular conduction resistance