论文部分内容阅读
目的探讨发作性运动诱发性运动障碍的临床特点。方法依据Demirkiran等的诊断标准对19例患者进行确诊,并对其临床资料进行分析。结果本组患者发病年龄为7~16岁,随年龄增长病情逐渐缓解;通常由突然随意运动后而出现,表现肢体(最常受累)、躯干、颈部或面部的肌张力障碍,持续数秒至数十秒,意识清楚;发作间歇期运动功能正常;发作期及间歇期脑电图、神经影像学检查多正常;对抗癫痫药物反应良好。结论发作性运动诱发性运动障碍是临床上较为少见的疾病,容易误诊,但临床疗效及预后良好。
Objective To investigate the clinical features of episodic motor-induced dyskinesia. Methods Based on the diagnostic criteria of Demirkiran et al, 19 patients were diagnosed and their clinical data were analyzed. Results The patient’s age at onset was 7-16 years old and gradually eased with age; it usually occurred after a sudden and voluntary exercise and manifested a dystonic, torso, neck or facial dystonia lasting several seconds Dozens of seconds, a clear consciousness; seizure intermittent motor function; seizure and intermittent EEG, neurological imaging examination more than normal; good response to epilepsy drugs. Conclusions The episodic motor-induced dyskinesia is a relatively rare clinical disease and is easily misdiagnosed. However, the clinical efficacy and prognosis are good.