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1973年至1985年间,波士顿儿童医院为生后1天~18个月(平均7个月)的220例法乐氏四联症(TOF)患儿施行纠治术。其中单纯TOF143例(69%),TOF伴其它畸形37例(20%),TOF伴肺动脉闭锁21例(11%)。手术在深低温心脏停搏下进行。术式有:补片跨在发育不全的肺动脉瓣环上(85%),右室至肺动脉间植入无瓣导管(4%),肺动脉瓣保留(11%)。术后30天内死亡17例(8%),包括:单纯TOF7例(5%),TOF伴其它畸形6例(16%),TOF伴肺动脉闭锁4例(19%)。即TOF伴肺动脉闭锁或其它畸形者术后早期死亡率高于单
Between 1973 and 1985, Boston Children’s Hospital performed corrective surgery in 220 children with tetralogy of Fallot (TOF) who were born between 1 and 18 months (mean, 7 months). Among them, TOF was found in only 143 cases (69%), TOF was associated with other abnormalities in 37 cases (20%), TOF with pulmonary atresia in 21 cases (11%). Surgery was performed under hypothermic cardiac arrest. Procedures were: patch across the hypoplasia of the pulmonary valve annulus (85%), between the right ventricle to the pulmonary artery implants without valve (4%), pulmonary valve retention (11%). Seven patients (8%) died within 30 days after surgery, including 7 cases of TOF (5%), 6 cases (16%) of TOF with other malformations and 4 cases (19%) of TOF with pulmonary atresia. That TOF with pulmonary atresia or other deformities were higher than the early postoperative mortality