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目的探讨原发性骨网状细胞肉瘤的临床及X线表现,以期提高对本病的诊断和鉴别诊断水平。方法结合临床表现、手术及病理所见回顾性分析经病理证实的11例原发性骨网状细胞肉瘤的X线特点。结果长管状骨5例(45%),椎骨、肋骨及骨盆各2例(各占18%)。主要X线改变为溶骨性破坏,有软组织肿块者7例,病理骨折1例,骨膜反应仅见2例且较轻微。结论当X线发现溶骨性恶性病变伴软组织肿块,且临床症状较其他骨恶性肿瘤为轻者,应考虑原发性骨网状细胞肉瘤的可能,最后确诊有赖于病理学证实。
Objective To investigate the clinical and X-ray findings of primary bone reticular cell sarcoma in order to improve the diagnosis and differential diagnosis of this disease. Methods According to the clinical manifestations, surgical and pathological findings, the pathological findings of 11 cases of primary bone reticular cell sarcoma were analyzed retrospectively. Results Long tubular bone in 5 cases (45%), vertebrae, ribs and pelvis in 2 cases (18% each). The main X-ray changes to osteolytic destruction, with soft tissue mass in 7 cases, pathological fracture in 1 case, only 2 cases of periosteal reaction and more minor. Conclusion When osteolytic malignancies are found in X-ray with soft-tissue mass and the clinical symptoms are lower than those in other malignant tumors, the possibility of primary osteoregional sarcoma should be considered. The final diagnosis depends on the pathological evidence.