腺泡状软组织肉瘤(alveolar soft tissue sarcoma,ASPS)是一种组织来源不明、细胞呈腺泡样或器官样排列的软组织恶性肿瘤。ASPS是一类罕见的软组织肉瘤类型,治疗上一般以手术为主,辅以术后放化疗,国内外关于靶向药物治疗的报道罕见。2015年10月12日我科收治1例大腿ASPS伴双肺转移的患者,服用阿帕替尼片治疗,疗效显著,现报道如下。 Alveolar soft tissue sarcoma (ASPS) is a kind of soft tissue malignant tumor whose source is unknown and whose cells are acinar-like or organ-like. ASPS is a rare type of soft tissue sarcoma, the treatment is generally based on surgery, combined with postoperative radiotherapy and chemotherapy, domestic and international reports on targeted drug treatment is rare. October 12, 2015 I treated one patient with thigh ASPS with lung metastases, taking apatinib tablets, the effect is significant, are reported below.