肾盂积水常见,但容量超过1000毫升以上的巨大型肾积水少见。据我们统计,自1952年到1964年国内已报告30例,1964年至1975年报导4例。但容量超过10000毫升以上的超巨大型肾盂积水更少见。我们曾遇到一例先天性左侧输尿管狭窄并发左肾超巨大型肾积水,误诊为卵巢囊肿。现报告如下,并讨论有关问题。 Hydronephrosis is common, but giant hydronephrosis, with volumes exceeding 1000 ml, is rare. According to our statistics, 30 cases were reported in China from 1952 to 1964, and 4 cases were reported from 1964 to 1975. However, the capacity of more than 10,000 ml of ultra-large hydronephrosis is even more rare. We have encountered a case of congenital left ureteral stricture of the left renal super giant hydronephrosis, misdiagnosed as ovarian cysts. We report the following and discuss the relevant issues.