Recently,we treated a patient with pulmonary vein sarcoma.The patient was a 41-year-old woman,had cough,short of breath and apsychia,with obvious jugular venous distention,rales in both lungs and a diastolic murmur at the apex.CT and Echo revealed a tumor in the left atrium.She received an emergency surgery to remove the mass in the heart.The pathological diagnosis demonstrated it as leiomyosarcoma.Though the patient accepted radiotherapy and chemotherapy,she still died of recurrence and metastasis of the sarcoma 10 months after operation.