作者报道了1例先天性小肠淋巴管扩张症CT表现为晕轮征病人。为男性,31岁,5岁时行小肠穿刺活检确定诊断,低脂及甘油三酯饮食治疗25年,无并发症。1991年形成难控制的乳糜性腹水,行LeVeen分流术。1992年7月全身肿胀并呼吸困难,住院前十天患者全身肿胀伴有进展性面部、上肢和 The authors reported 1 case of congenital small intestine lymphangiectasis CT showed halo wheel sign patients. For men, 31 years old, 5 years old to confirm the diagnosis of small intestine biopsy, low-fat and triglyceride diet for 25 years, no complications. In 1991 the formation of refractory chylous ascites, line LeVeen shunt. July 1992 Swelling and breathing difficulties, ten days before admission, patients with systemic swelling associated with progressive facial, upper extremity and