目的研究特发性低颅压综合征（ＳＩＨ）的临床特点及特征性影像学所见。方法对１年１１个月间收治的８例ＳＩＨ患者，详细观察其临床特点，多次腰穿检测其脑脊液（ＣＳＦ）压力及生化学、头ＣＴ、ＭＲＩ平扫和Ｇｄ－ＤＴＰＡ增强扫描。结果当患者出现起立性头痛、呕吐、颈强直时，其脑压≤０．７ｋＰａ。其中５例呈血性ＣＳＦ，７例蛋白增高，似蛛网膜下腔出血（ＳＡＨ）。ＣＴ示脑室缩小，ＭＲＩ增强扫描示硬脑膜强化，硬膜下积液和特异性脑髓下垂之改变。当其临床症状消退时，其脑压及ＣＳＦ生化学恢复正常。结论了解ＳＩＨ的临床及ＭＲＩ的特异性改变对于正确诊断和治疗ＳＩＨ至关重要，以防误诊 Objective To study the clinical features and characteristic imaging findings of idiopathic low intracranial pressure syndrome (SIH). Methods Eight patients with SIH who were treated in one year and 11 months were enrolled in this study. Their clinical features were observed in detail. CSF pressure and biochemistry, head CT, MRI plain scan and Gd-DTPA enhanced scan were performed by multiple lumbar puncture. Results When patients with standing headache, vomiting, neck stiffness, the brain pressure ≤ 0.7kPa. Five of them were bloody CSF and seven had protein hypersecretion, similar to subarachnoid hemorrhage (SAH). CT showed ventricular contraction, MRI enhanced scan showed dura mater, subdural effusion and specific changes in pterygia. When its clinical symptoms subsided, its brain pressure and CSF biochemistry returned to normal. Conclusions Understanding the clinical and MRI-specific changes in SIH is crucial for the correct diagnosis and treatment of SIH to prevent misdiagnosis