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重症联合免疫缺陷病(简称SCID)是代表一组体液和细胞免疫严重缺陷的综合征。此病常在生后3个月开始起病,不予治疗时,大多在2岁内死亡。国外对此病进行了较多的研究,深入探讨了此病的发病机制及治疗。国内近几年来也陆续有个案报导。有人报导在加拿大某地的印地安人SCID的发病率,活产婴儿中大约为1/3000,而远亲婚配的高加索人,为活产婴儿的1/300,000。在瑞典联合免疫缺陷病占原发性免疫缺陷病的20.8%。也有报导为10～25%,而SCID则占原发性免疫缺陷病的4.6%。合屋统计了日本1966～1975年628例原发性免疫缺陷病,26例为SCID
Severe combined immunodeficiency disease (SCID) is a syndrome that represents a group of severe defects in humoral and cellular immunity. The disease often onset 3 months after birth, when not treated, mostly within 2 years of age died. More foreign studies on the disease, in-depth discussion of the pathogenesis and treatment of the disease. In recent years, there have also been case reports in China. It has been reported that the incidence of Indian SCIDs in some parts of Canada is about 1/3000 for live births and 1 / 300,000 for far-fetched males. In Sweden, combined immunodeficiency disease accounts for 20.8% of primary immunodeficiency disease. There are also reports of 10 to 25%, while SCID accounts for 4.6% of the primary immunodeficiency disease. The house statistics 628 cases of Japanese primary immunodeficiency disease from 1966 to 1975, 26 cases of SCID