论文部分内容阅读
目的分析少见的平山病(Hirayama disease,HD),就其临床、影像学特点及发病机制进行探讨,提高对该病的认识。方法采用回顾行研究方法,报告1例曾误诊为运动神经元病的平山病的临床表现及检查资料。结果该病例为男性,青春期发病,呈单侧上肢远端无力伴萎缩;肌电图为神经源性改变,屈颈MRI可见下段颈髓前移、硬脊膜向前移位,硬膜外间隙增宽。结论根据平山病的临床及屈颈位MRI表现的特点,可以提高确诊率。
Objective To analyze the rare Hirayama disease (HD) and discuss its clinical features, imaging features and pathogenesis to improve its understanding of the disease. Methods The retrospective research methods were used to report the clinical manifestations and examination data of 1 case of Pingshan disease that had been misdiagnosed as motor neuron disease. Results The case was male, with onset of adolescence, distal unilateral weakness accompanied by atrophy; EMG neurogenic changes, lower cervical spinal cord MRI can be seen in advance, dural forward forward displacement, epidural space Widening. Conclusion According to the clinical features of Pingshan disease and the features of MRI manifestations of flexor cervical flexion, the diagnosis rate can be improved.