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纯红细胞再生障碍性贫血(PRCA)是再障贫血的一种特殊类型,是以骨髓中仅有单纯红细胞系统造血衰竭为特征的一组疾病。我院1987~1989年收治68例慢性肾炎中,合并PRCA12例,报道如下。1 临床资料1.1 性别与年龄 男5例,女7例。年龄24~58岁,平均41岁。病程3~12年,平均8年;肾功能代偿期1例,氮质血症期3例,尿毒症期8例。临床表现:均以水肿伴头昏、乏力为主诉;6例牙龈出血、呕吐、皮肤搔痒,均为尿毒症期患者。本组均无酱油样尿。病前2例曾服氯霉素。体查:4例血压增高,最高28/16.8kPa,余血压正常。均重度贫血
Pure red cell aplasia (PRCA) is a special type of aplastic anemia, a group of diseases characterized by hematopoietic failure of the pure erythrocyte system in the bone marrow. 68 cases of chronic nephritis admitted to our hospital from 1987 to 1989, combined with PRCA in 12 cases, reported as follows. 1 Clinical data 1.1 Sex and age 5 males and 7 females. Aged 24 to 58 years old, average 41 years old. Course of 3 to 12 years, an average of 8 years; 1 case of renal decompensation, azotemia in 3 cases, uremia in 8 cases. Clinical manifestations: all edema with dizziness, fatigue mainly complaints; 6 cases of bleeding gums, vomiting, itchy skin, are patients with uremia. This group are no soy sauce-like urine. 2 cases before taking chloramphenicol. Physical examination: 4 cases of elevated blood pressure, the highest 28 / 16.8kPa, more than normal blood pressure. Both have severe anemia