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结节性硬化症(TS)伴癫痫的患儿,智力通常低下,其认知和行为表现与其临床和神经放射学方面的关系,尚未见报道。病人和方法该文作者于1986~1987年,诊断了23例 TS 患儿,男15例,女8例,随访至少3年。对所有病儿进行标准化的心理测验和认知功能的评估,结果用智商(IQ)或发育商(DQ)表示。根据 DSM-Ⅲ-R 标准来诊断智力低下和行为障碍。根据 TS 行为调查表来诊断孤独症。对所有病儿进行磁共振成像(MRI)检查。
Children with tuberous sclerosis (TS) and epilepsy usually have low intelligence and no relationship has been reported with their clinical and neuroradiological findings regarding their cognitive and behavioral manifestations. PATIENTS AND METHODS The author diagnosed 23 children with TS from 1986 to 1987, 15 males and 8 females, who were followed up for at least 3 years. Standardized sickness tests and assessment of cognitive function were performed on all sick children and the results were expressed as IQ or DQ. Diagnose mental retardation and behavioral disorders according to DSM-III-R criteria. According to TS behavior questionnaire to diagnose autism. All sick children were examined by magnetic resonance imaging (MRI).