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患儿男,12岁。小肠部分切除术后反复腹痛3月。患者3月前突发腹痛伴呕吐,疼痛为持续性,阵发性加剧,经当地医院观察24h后急诊手术,术中见空肠套叠,套叠远端有一包块。将套叠复位,把远端包块内的部分小肠切除吻合,当地医院病理诊断:小肠乳头状瘤。术后偶感腹痛,呕吐,以小肠肿瘤收住我院。查体:患者5岁时口唇周围、口腔粘膜、双手指、足趾掌面见有黑褐色斑点,不痛,不痒,不突出皮面,始终未退。家族中无遗传病史。右腹脐旁可见10cm切口瘢痕,于右上腹可及一约10cm×6cm之包块,游动、质软,有触痛,X线钡餐造影:①空肠上中段肠套工,②小肠中段肿瘤。
Children male, 12 years old. Intestinal pain after repeated partial abdominal resection in March. Patients with sudden abdominal pain and vomiting 3 months ago, the pain was persistent, increased paroxysmal, observed by the local hospital after emergency surgery 24 hours, surgery see jejunum intussusception, intussusception in the distal have a mass. The telescopic reduction, the distal mass within the small intestine resection and anastomosis, the local hospital pathological diagnosis: enteric papilloma. Occasionally suspected abdominal pain, vomiting, admitted to our hospital with small bowel cancer. Physical examination: 5 years old patients around the lips, oral mucosa, both fingers, toe palms see dark brown spots, no pain, no itch, not prominent leather, never back. Family history of no genetic disease. The right abdomen umbilical visible 10cm incision scar in the right upper quadrant can be about a 10cm × 6cm mass, swimming, soft, tenderness, X-ray barium meal angiography: ① upper jejunum intestine intussusception, ② middle small intestine tumor .