朗格汉斯组织细胞增多症(Langerhans’cell histiocy tosis,LCH)是一组原因末明的组织细胞增生性疾患,朗格汉斯细胞(LC)增生是共同的组织病理学特点,而临床上是一组异质性疾病,过去称组织细胞增生症X。该病在小儿并非罕见,因其临床表现各异。且不典型,故临床诊断困难。1临床资料患儿,女,11月龄,因“反复发热半年余”入 Langerhans’ histiocytosis (LCH) is a group of histopathogenic disorders of unknown origin. Langerhans cell (LC) hyperplasia is a common histopathological feature, and clinically Is a heterogeneous group of diseases, formerly known as histiocytosis X. The disease is not uncommon in children because of its different clinical manifestations. And not typical, so the clinical diagnosis is difficult. 1 clinical data of children, women, 11 months old, because of “repeated fever more than six months,” into