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患者男性,32岁,发作性室性心动过速4年,曾多次经药物及电击复律.1993年2月1日,因室速再发Zh入院.BP110/75mmHg(14.5 /10.0kPa),面色苍白,口唇发绀,颈静脉无怒张,心界不大,心率180次/min.心电图示左束支阻滞型室速(图略).立即给利多卡因50mg稀释后静推转为窦性,心率80次/min,症状好转.次日心电图示窦性心律,不完全右束支阻滞(图略).心脏超声检查见右心室扩大,游离壁变薄,上半部向外膨出.心尖四腔图示右室49×72mm,诊断致心律失常性右室发育不全.
Male, 32 years old, paroxysmal ventricular tachycardia for 4 years, has repeatedly by the drug and electric shock cardioversion .In February 1, 1993, due to retrospective ventricular tachyphnia admission .BP110 / 75mmHg (14.5 /10.0kPa) , Pale, lips cyanosis, jugular vein without rage, heart, heart rate 180 beats / min. ECG left bundle branch block-type ventricular tachycardia immediately after lidocaine 50mg intravenously diluted For sinus, heart rate 80 beats / min, the symptoms improved.The next electrocardiogram shows sinus rhythm, incomplete right bundle branch block (Figure omitted.) Echocardiography showed right ventricular enlargement, free wall thinning, the upper half to Bulging outside the apical four chamber icon right 49 × 72mm, diagnosis of arrhythmogenic right ventricular hypoplasia.