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具有内分泌功能的胰腺肿瘤称为APU-Doma。本文报告病例是分泌“作用于血管的肠多肽(VIP)胰腺APUDoma”。临床表现水泻、低血钾及胃酸缺乏,即所谓WD-HA 症候群。本病例胰内还长着无内分泌功能的类癌。生长APUDoma 的胰腺细胞,属于神经嵴细胞类。这类细胞主要功能是分泌过多的胺前物质(如多肽),并能脱羧基,英文缩写为APUD。“APUD 细胞并非仅见于胰腺,它分布在人体各处,因而在许多器
A pancreatic tumor with endocrine function is called APU-Doma. The case reported here is the secretion of “VIP pancreatic APUDoma” from the blood vessels. Clinical manifestations of water diarrhea, hypokalemia and gastric acid deficiency, the so-called WD-HA syndrome. In this case, there is also a carcinoid without endocrine function in the pancreas. Growth of APUDoma’s pancreatic cells belongs to the neural crest cell class. The main function of these cells is to secrete excessive amounts of amine pro-forms (such as peptides) and to decarboxylate them, abbreviated as APUD in English. "APUD cells are not only found in the pancreas. It is distributed throughout the body and therefore in many devices.