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目的探讨小儿复发性呼吸道乳头状瘤病(JORRP)喉阻塞的外科治疗特点。方法回顾性分析我科收治并进行反复外科治疗的JORRP所致喉阻塞患儿13例临床资料。结果 JORRP首次诊断平均年龄1.6岁,喉阻塞平均发病年龄3.8岁,平均手术3.5次,平均复发时间7个月,术后并发喉功能障碍8例,气管切开11例,1例气管造口有乳头状瘤播散。结论 JORRP是儿童最常见的喉部肿瘤,由于易复发,常需多次手术,而且容易引起喉阻塞,危及生命,手术应注意保存喉部正常组织结构,常需气管切开解除呼吸道阻塞,还要防治病变局部接种和邻近器官传播。
Objective To investigate the surgical treatment of childhood recurrent respiratory papillomatosis (JORRP) laryngeal obstruction. Methods Retrospective analysis of 13 cases of children with throat obstruction caused by JORRP in our department for repeated surgical treatment. Results The mean age of first diagnosis of JORRP was 1.6 years. The average age of onset of laryngeal obstruction was 3.8 years. The average operation time was 3.5 and the average recurrence time was 7 months. There were 8 cases of laryngeal dysfunction, 11 cases of tracheotomy and 1 case of tracheostoma Papilloma spreads. Conclusion JORRP is the most common laryngeal tumor in children. Due to its easy recurrence, JORRP often requires multiple surgeries and can easily lead to laryngeal obstruction and endanger life. Surgical care should be taken to preserve the normal tissue structure of the larynx. Tracheostomy is often required to relieve airway obstruction. To prevent and treat local lesions and spread of adjacent organs.