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众所周知,肺血管病变是多种先天性心脏病最严重的合并症之一,矫形手术后患儿血液循环能否恢复正常在很大程度上取决于肺血管的病变程度。因此,先天性心脏病肺血管病变的研究将为临床选择手术时机及估计预后提供形态学依据。我们对23例先天性心脏病时的肺血管改变作了观察。材料和方法23例中室间隔缺损8例,室间隔缺损合并其他畸形9例,房间隔缺损(房缺)6例。每例两肺各叶至少取一块组织作石蜡切片,HE染色,Van Gieson染色及Verhoeff’s弹力纤维染色,观察计数所有10μm以上肺小动脉。肺小动脉病变以日本Yamaki分类法进行分类计数。病变分四级。Ⅰ级:中膜平滑肌增生,无血管内膜反应;Ⅱ级:内膜细胞反应;Ⅲ
As we all know, pulmonary vascular disease is one of the most serious complications of congenital heart disease, orthopedic surgery in children with blood circulation to return to normal depends largely on the degree of pulmonary vascular disease. Therefore, the study of pulmonary vascular disease of congenital heart disease will provide the morphological basis for clinical choice of operation timing and prognosis. We observed 23 cases of pulmonary vascular changes during congenital heart disease. Materials and Methods 23 cases of ventricular septal defect in 8 cases, ventricular septal defect combined with other deformities in 9 cases, atrial septal defect (atrial septal defect) in 6 cases. At least one piece of tissue was taken from each of the two lungs for paraffin sections, HE staining, Van Gieson staining and Verhoeff’s elastic fiber staining. All the pulmonary arterioles above 10 μm were observed and counted. Pulmonary arterioles lesions were classified by Japanese Yamaki classification. Lesions at four levels. Grade I: Mesothelial smooth muscle hyperplasia, no vascular intimal reaction; Grade II: endometrial cell response; III