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重症肌无力是一种神经肌肉接头间传递功能障碍的疾病,主要表现为受累横纹肌极易疲劳,休息后或给抗胆碱酯酶药物后恢复。该病与免疫和内分泌有密切关系,现报告2例眼肌型重症肌无力误行眼睑切除。例1 男性:70岁。因睁眼费力右眼睑下垂6个月入院。6月前无诱因出现睁眼费力,2月后右眼睑下垂眼裂变窄约2~5mm。病后3月症状加重行右眼睑切除术,术后病情改善,3个月后又出现左眼睑下垂,同时伴嚼咬无力而入院。既往患风心病。神经系统检查颅神经仅可见双眼睑下垂,左重于右,睁闭眼疲劳试验阳性,双嚼咬叽、咽肌轻度无力,其余检查正常。空腹血糖83mg%,T_3135ng%,T_410μg%,血免疫球蛋白(?)gG13.5mg/ml,IgA2.92
Myasthenia gravis is a disorder of transmission between neuromuscular junction dysfunction, mainly manifested as fatigue easily affected by rhabdomyolysis, or after resuscitation to anticholinesterase drugs. The disease is closely related to the immune and endocrine, is reported in 2 cases of ocular myasthenia gravis misoperation eyelid resection. Example 1 Male: 70 years old. Due to eyes open drooping right eyelid 6 months admitted. There was no incentive to appear 6 months ago, eyes open and effort, in February after the right eyelid ptosis narrowed about 2 ~ 5mm. After the illness in March to aggravate the symptoms of right eyelid resection, postoperative condition improved, 3 months after the left eyelid ptosis, accompanied by bite weakness and hospitalization. Past wind disease. Nervous system examination of cranial nerves visible only double eyelid ptosis, left heavier than the right, eyes open eye fatigue test positive, double chew biting grumble, pharyngitis mild weakness, the rest of the examination was normal. Fasting blood glucose 83mg%, T_3135ng%, T_410μg%, blood immunoglobulin (?) GG13.5mg / ml, IgA2.92