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Mobius综合症是临床上较为罕见的以双例面瘫为主,伴有其他器官畸形的一种疾病。复习国内外文献,国外早有人报告,但国内、仅见1981年李鸿智等报告过三例。现将我们遇到的二例报告如下: 例1 男,16岁。主诉面无表情伴小口14年,要求整容而入院。病人出生后能免强吸吮,但直到2岁未见哭笑面容,且发现口唇未再发育。2岁前曾患过面部疱疹(当时诊断不祥)。查体:发育一般,智力尚可、面无表情,呈假面具样面容,两眼裂较大,
Mobius syndrome is clinically rare in patients with double facial paralysis, accompanied by other organ deformities of a disease. Review of the literature at home and abroad, early foreign reports, but in China, only seen in 1981, Li Hongzhi and other reports in three cases. Now we have two cases reported as follows: Example 1 Male, 16 years old. Main facial expression with no expression with a small mouth for 14 years, requiring plastic surgery and admission. After the birth of the patient can avoid sucking, but until the age of 2 did not see the laughing face, and found no further development of the lips. 2 years ago had had facial herpes (was diagnosed ominously). Physical examination: general development, intelligence is acceptable, expressionless, was a mask-like face, split the larger eyes,