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作者根据1986~1996年间收集的有关脑静脉畸形的临床信息来确定脑出血的危险性和发生率以及与脑静脉畸形有关的死亡率。10年间共观察了80例,总观察人次是1100人。通过血管造影和磁共振进行诊断,确诊后注册登记。以调查表或电话等形式获得临床信息。 80例中,男39例,女41例,平均年龄38岁。22例表现为与脑静脉畸形有关的神经症状和体征:头痛的9例,癫痫发作的4例,感觉异常及运动障碍的各3例,三叉神经痛的2例,锥体外系功能障碍的1例。23例表现为与脑静脉畸形无关的头痛。脑静脉畸形大多发生在颅后窝。发生在脑干的7例,在大脑半球或肿瘤茎部的29例,在脑皮质的28例,在脑实质深层的白质内10例,在基底节的3例,在丘脑的2例,在三角区的1例。除脑静脉畸形外,14例伴有脑内病理性异常。
The authors determined the risk and incidence of cerebral hemorrhage and the mortality associated with cerebral venous malformations based on clinical information collected from 1986 to 1996 on cerebral venous malformations. A total of 80 cases were observed in 10 years and the total number of observers was 1,100. Diagnosed by angiography and magnetic resonance, diagnosed after registration. Get clinical information in the form of questionnaires or phone calls. In 80 cases, 39 males and 41 females, with an average age of 38 years. Twenty-two patients showed neurological symptoms and signs associated with cerebral venous malformations: 9 cases of headache, 4 cases of seizures, 3 cases of sensory abnormalities and dyskinesias, 2 cases of trigeminal neuralgia, 1 cases of extrapyramidal disorders example. 23 cases showed headache unrelated to cerebral venous malformations. Cerebral venous malformations occur mostly in the posterior fossa. Seven cases occurred in the brain stem, 29 in the cerebral hemispheres or tumor stems, 28 in the cortex, 10 in the deep white matter of the parenchyma, 3 in the basal ganglia and 2 in the thalamus, One case of triangular area. In addition to cerebral venous malformations, 14 cases associated with pathological brain abnormalities.