儿童的一些肾病与囊肿发生相关,双侧巨大囊肾通常系常染色体隐性或显性遗传多囊肾病或结节性硬化所致。本文作者介绍3例。患者1,男,6个月时见重度腹部膨隆,查体双肾肿块,高血压(155/70mmHg)和3处色素减少斑。经静脉肾孟造影诊断为显性遗传多囊肾病,其父母肾影像检查正常,经咨询患儿属散发病例,12个月时因持续高热,惊厥1小时而入院,血压为230/100mmHg,用心得安和克 Some children’s nephropathy is associated with the occurrence of cysts. Bilateral giant cystic nephrosis is usually caused by autosomal recessive or dominant genetic polycystic kidney disease or tuberous sclerosis. The author introduces 3 cases. Patients 1, male, 6 months, see severe abdominal bulge, check the body mass, hypertension (155 / 70mmHg) and three pigmentation spots. The diagnosis of renal pelvis and phonocardiography was dominant genetic polycystic kidney disease, whose parents had normal renal imaging. The patients were diagnosed as having sporadic cases. At 12 months, the patients were hospitalized with convulsions for 1 hour at 12 months. The blood pressure was 230 / 100mmHg, Experience and peace