嗜血细胞综合征亦称嗜血细胞性淋巴组织细胞增生症(HPG),1979年首先由Risdall等报道,分为原发性和继发性两类,前者为常染色体隐性遗传病,后者可由感染、免疫或肿瘤所致[1]。嗜血细胞综合征的诊断标准如下:发热超过1周,热峰≥38.5℃;肝脾肿大,全血细胞减少,累及≥2 Haemophilus syndrome, also known as hemophagocytic lymphohistiocytosis (HPG), first reported in 1979 by Risdall et al., Is divided into two types of primary and secondary, the former is autosomal recessive disease, the latter by Infection, immunity or cancer caused by [1]. Diagnostic criteria for hemophilia syndrome are as follows: fever over 1 week, heat peak ≥ 38.5 ℃; hepatosplenomegaly, pancytopenia, involving ≥ 2