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本文报道了新疆8个家系共13例G组异常Hb,均经结构分析,证实此种变异体为HbGTaipei[β22(B_4)Glu→Gly],其中2例维吾尔、哈萨克族HbGTaipei在我国系首次报道。对本组资料进行了生化和血液学研究,并对HbGTaipei的分布、起源及其人类学意义等进行了讨论。
In this paper, we report 13 abnormal Gb HbGTaipei from 8 Chinese families in Xinjiang, all of which were confirmed by structural analysis. HbGTaipei [β22 (B_4) Glu → Gly] was confirmed in these 8 families. Two Uighur and Kazakh HbGTaipei were reported in our country for the first time . Biochemical and hematological studies were conducted on this group of data, and the distribution, origin and anthropological significance of HbGTaipei were discussed.