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1890年Groenouw首先报遭两例遗传性角膜营养不良,其中有一例为斑状角膜营养不良(macular corneal dystrophy),故又称为GroenouwⅡ型角膜营养不良。1938年Buckler报道:13个家系800人中,有角膜营养不良者共129人,其中颗粒状者91人;斑状者32人;格子样者6人。故本病亦称:BucklerⅡ型角膜营养不良。近年来我国亦有本病病例及家系调查报告。但仍未有病理组织学及超微结构的研究报道。我院于1982年收治一例,施行部分穿透性角膜移植术,将取下的病变角膜进行病理组织学检查,今报道如下: 病例:曹××,男性,43岁,工人,因双眼视力逐渐下降,角膜出现斑片状混浊20年,于1982年11月20日入院。现病史:患者23岁时开始双眼视力下降,角膜中部有点状白色混浊,以后扩大融合,最后中央部呈云雾状,34岁时双眼视力为
In 1890 Groenouw first reported two cases of hereditary corneal dystrophy, one case of macular corneal dystrophy, it is also known as Groenouw type Ⅱ Corneal dystrophy. In 1938, Buckler reported that there were 129 corneal malnutrition among the 800 people in the family of 13, among which 91 were grainy, 32 were macular, and 6 were plaid. So the disease is also known as: Buckler type Ⅱ Corneal dystrophy. In recent years, our country also has the disease cases and pedigree investigation report. However, there are still no reports of histopathological and ultrastructural studies. Our hospital was admitted to a case in 1982, the implementation of some penetrating keratoplasty, removal of diseased corneal histopathological examination, reported as follows: Case: Cao × ×, male, 43 years old, workers, due to binocular vision gradually Declining corneal patchy opacity 20 years, in November 20, 1982 admission. Current history: The patient began to reduce binocular vision at the age of 23, the cornea a little bit white turbid later expanded fusion, the central part was cloud-like, 34-year-old binocular vision was