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血红蛋白H(HbH)病首先在海外华侨中发现,近年来证明国内华南地区并非少见(1)。但青海地区至今尚未见有本病之报导,现将我院发现的一例报告于后,供参考。病例报告患者李××,男,39岁,汉族,青海省互助士族自治县人。父母及祖父母均世居于青海互助。患者自1974年10月以来,感全身疲乏无力,头晕,曾在我省数医院诊断为溶血性贫血、脾功能亢进症及早期肝硬
Hemoglobin H (HbH) disease was firstly found in overseas Chinese and it has been proved in recent years that it is not uncommon in South China (1). However, no reports of this disease have yet been found in Qinghai Province, and one case report found in our hospital is for reference later. Case Report Patients Li × ×, male, 39 years old, Han nationality, Qinghai Province mutual aid people Autonomous County people. Parents and grandparents live in mutual assistance in Qinghai Province. Patients since October 1974, feeling full body fatigue, dizziness, several hospitals in our province have been diagnosed as hemolytic anemia, hypersplenism and early liver cirrhosis