论文部分内容阅读
先天性束带综合症(congenital constricting band syndrome,CCBS)为临床少见病种,出生时可见完全性或不完全性环绕肢体软组织的凹陷,多发于小腿,足趾、前臂、手指,偶尔在躯干亦有发现,可同时伴肢体畸形。手术方法是彻底松解束带,做对偶皮瓣Z字成形。传统的观点认为束带要分2~3期手术,以防止皮瓣坏死和影响肢体血运,随着医疗水平的提高,技术方法的不断改进,1期手术直接做Z字成形松解完全可能,减少了手术次数,缩短了治疗时间,使获得良好的发育。“,”Congenital band syndrome (congenital constricting band syndrome, CCBS) for clinical rare disease, birth is complete or incomplete around the limb soft tissue sag, happens in the calf, toes, forearm and finger, occasional y in the trunk has also found that can accompany limb deformities at the same time. Surgical method is completely loose XieShu belt, Z forming dual flap. The traditional view that band to 2~3 phase of the operation, in order to prevent the skin flap necrosis and af ected limb blood supply, along with the improvement of medical standards, continuous improvement of technical methods, 1 surgery done directly Z forming loose solution is possible, to reduce the operation rate, shorten the treatment time, make good development.