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中心性网状脉络膜营养不良是以慢性进行为特征的视网膜色素上皮和脉络膜毛细血管网的局限性萎缩,属于常染色体显性或隐性遗传性疾病。一般认为本病与以往报道的中心性脉络膜硬化、中心性脉络膜血管萎缩、中心性进行性网状脉络膜营养不良为同一种疾病。临床上又称为中心性轮状脉络膜萎缩。发病年龄多在成年期。本病国内报告甚少。现将我院近几年经荧光血管造影、眼电生理检查后诊断为本病的9例报告如下。本文9例中男3例、女6例,就诊年龄最小18岁,最大55岁,平均37.3岁,病程最长30余年,最短3年。病变位于中心凹者8例,另外1例一眼位于
Central reticular choroidal dystrophy is a localized atrophy of the chronic retinal pigment epithelium and chorioretinal network characterized by autosomal dominant or recessive inherited disease. It is generally believed that the disease with the previously reported central choroidal sclerosis, central choroidal vasoconstriction, central progressive reticular choroidal dystrophy for the same disease. Clinically also known as central atrioventricular atrophy. Age of onset in adulthood. Domestic reports of this disease is poor. Now in our hospital by fluorescent angiography in recent years, electrophysiology after diagnosis of the disease reported in 9 cases as follows. 9 cases in this paper, 3 males and 6 females, the youngest age of 18 years, maximum 55 years old, average 37.3 years, the longest duration of more than 30 years, the shortest of 3 years. 8 cases of lesions located in the fovea, the other one case located in one