论文部分内容阅读
非典型性溶血尿毒综合征(atypical hemolytic uremic syndrome,aHUS)是血栓性微血管病(thrombotic microangiopathy,TMA)中的一种疾病,临床上比较少见,在北美人群的发病率约为2/(百万人·年)〔1〕。长期以来aHUS未被人们了解与重视,将之归属为HUS,称为家族性HUS。HUS与aHUS的临床特征都表现为“三联征”:微
Atypical hemolysis uremic syndrome (aHUS) is a disease of thrombotic microangiopathy (TMA), which is rare in clinic. The incidence in North American population is about 2 / (million Person · years) 〔1〕. For a long time, aHUS has not been known and valued by people. It belongs to HUS and is called familial HUS. The clinical features of both HUS and aHUS are shown as “triple sign”: micro