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当今世界上对胆道闭锁的治疗有两种方式:肝门肠吻合(Kasai手术)或肝移植。自从1959年日本Kasai对首例胆道闭锁行肝门空肠吻合术以来,经过近40年来的临床实践确实有一部分患儿得以长期生存,其中不乏生活质量近乎正常儿童的患儿。也有一部分出现了各种晚期
There are two ways to treat biliary atresia in the world today: hepatectomy (Kasai surgery) or liver transplantation. Since the first biliary atretic hysterosalpingogenesis in Japan by Kasai in 1959, there are indeed some patients with long-term survival after nearly 40 years of clinical practice, many of whom have children with almost normal quality of life. There are also a variety of late appeared