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目的 探讨手足局限型腱鞘巨细胞瘤MRI表现的病理学基础.方法 对21例病理确诊的局限型腱鞘巨细胞瘤(giant cell tumor of tendon sheath,GCTTS)MRI表现和病理特点进行回顾性分析.结果 T1加权像(T1ⅥI)表现为等信号13例,均匀低信号5例,等低混杂信号3例;T2加权像(T2WI)表现为高低混杂信号16例,不均匀等低信号3例,高信号2例;14例肿瘤边缘可见线状完整或不完整低信号影,7例相邻骨质压迫性吸收.其中15例患者行增强扫描,明显不均匀强化9例,明显均匀强化4例,轻度不均匀强化2例.结论 局限型GCCTS MRI表现具有特征性,MRI对于发现特异性含铁血黄素信号和确定病变范围具有独特优势,是目前诊断局限型GCTTS的首选方法.“,”Objective To evaluate the pathological basis of magnetic resonance imaging appearances of localized giant cell tumor of tendon sheath (L-GCTTS) in extremities.Methods The MRI image appearances and pathological characteristics of 21 patients with confinmed L-GCTTS were retrospectively reviewed.Results The signal intensities of L-GCTTS in T1 weighted images (T1WI) were isointense in 13 cases,even low signal in 5 cases and heterogeneously iso/hypo-intense in 3 cases.In T2 weighted images (T2WI),the signal was heterogeneously hyper/hypo-intense in 16 cases,uneven low signal in 3 cases and hyperintense in 2 cases.Complete or incomplete linear low signals of the capsules were displayed around the tumor in 14 patients.Images of 7 cases showed adjacent compressive bony absorption.There were 9 cases with heterogeneous marked enhancement,4 cases with homogeneous marked enhancement and 2 cases with heterogeneous mild enhancement of the 15 cases that had MRI enhancement scanning.Conclusion MRI appearances can reflect the pathological characteristics of L-GCTTS.MRI has a unique advantage to find specific hemosiderin signal and determine the extent of the lesion.MRI is the preferred way to diagnose L-GCTTS.