目的:探讨肾上腺皮质嗜酸细胞瘤临床、病理学特征及治疗方法。方法:报告1例肾上腺皮质嗜酸细胞瘤患者临床资料并复习文献。结果:患者临床表现库欣综合症,皮质醇节律异常,腹部CT示左肾上腺肿瘤,行后腹腔镜下肿瘤切除手术,术后病理证实为肾上腺皮质嗜酸细胞瘤。术后随访12个月,患者未见肿瘤复发和转移。结论:肾上腺皮质嗜酸细胞瘤临床罕见,大部分为偶发瘤。良性肿瘤多见,手术切除肿瘤为首选治疗,预后良好。 Objective: To investigate the clinical and pathological characteristics and treatment of adrenal cortex oncocytoma. Methods: The clinical data of 1 adrenocortical oncocytoma were reviewed and reviewed. Results: The clinical manifestations of Cushing’s syndrome, abnormal cortisol rhythm, abdominal CT showed left adrenal tumors, laparoscopic resection of the tumor, postoperative pathology confirmed adrenocortical oncocytoma. All the patients were followed up for 12 months without recurrence and metastasis of the tumor. Conclusion: Adrenal cortical oncocytoma is rare in clinic, and most of them are sporadic tumors. More common benign tumors, surgical removal of the tumor is the preferred treatment, the prognosis is good.