作者报道1个家族性常染色体显性卒中样发作和白质脑病综合征。45个成员中发现9个有短暂性脑缺血发作和卒中,神经放射学证实为小的深部梗塞和广泛性白质脑病,还有8个成员无临床症状,但神经放射学检查有相同的改变。现报道1例有临床症状死亡的病理变化。患者女,40岁。1971年开始癫痫大发作。1983年11月,突然右手麻木无力,构音障碍。1年后表情淡漠,情绪低落。1985年, The authors report a familial autosomal dominant stroke-like stroke and leukoencephalopathy syndrome. Nine of the 45 patients had transient ischemic attacks and strokes, deep neurolepties confirmed as small and extensive leukoencephalopathy, and eight had no clinical symptoms but had the same changes in neuroradiology . It is reported that 1 case of clinical symptoms of pathological changes. Female patient, 40 years old. 1971 onset of epileptic seizures. November 1983, suddenly his right hand numbness, dysarthria. 1 year after the expression of indifference, depression. In 1985,