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Von Hipple-Lindau病(VHL)是一种常染色体遗传性疾病,由染色体3p25的抑癌基因缺失或突变造成[1]。我科收治一位VHLII型患者,表现为双肾嗜铬细胞瘤及延髓血管母细胞瘤,行
Von Hipple-Lindau’s disease (VHL) is an autosomal genetic disorder caused by the deletion or mutation of the tumor suppressor gene on chromosome 3p25 [1]. Our department admitted to a VHLII patients, manifested as renal pheochromocytoma and medullary hemangioblastoma, line