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原发性心内膜弹力纤维增生症(EFE)是小儿心脏猝死的原因之一。目前认为由胎儿期或生后病毒感染引起,现将我院近几年收治的3例报告如下。病例摘要例1:女患,6个月系足月第一产,母孕三个月患过感冒。本人生后一周感冒一次。此次因发热伴气促2天入院。体温38℃,呼吸40次/分,脉搏160次/分,发育正常,营养佳,唇无发绀,心音纯,心率160次/分,律整,两肺正常,肝肋下1.0cm。心电图:双心室肥厚。入院后因反复心衰经抢救无效死亡。死后尸解:心内膜高度增厚,心室高度扩张。病理诊断为:急性型心内膜弹力纤维增生症。
Primary endocardial fibroelastosis (EFE) is one of the causes of sudden cardiac death in children. Currently considered by the fetus or postnatal virus infection, now my hospital admitted in recent years, three cases are as follows. Case Summary Example 1: Female patients, 6 months of full-term first trimester, pregnant women have had a cold for three months. I have a cold once a week after my birth. The fever with gas promote 2 days admission. Body temperature 38 ℃, breathing 40 beats / min, pulse 160 beats / min, normal development, good nutrition, lip cyanosis, pure heart sound, heart rate 160 beats / min, law, lungs normal, liver ribs 1.0cm. Electrocardiogram: Biventricular hypertrophy. After admission due to repeated heart failure by the rescue died. Postmortem autopsy: endocardial thickening, ventricular height expansion. Pathological diagnosis: acute endocardial fibroelastosis.