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目的探讨结外指突状树突细胞肉瘤的诊断要点及其鉴别诊断。方法对1例结外指突状树突细胞肉瘤进行组织病理学、免疫组化染色,并随访。结果肿瘤发生于肝脏、脾脏,于确诊4个月后死亡。镜检:肿瘤组织呈席纹状、旋涡状或杂乱排列,瘤细胞卵圆形、梭形,胞质少,核卵圆形或短梭形,染色质少,部分有核仁,分裂象多见。瘤细胞S-100、CD68、Vimentin和LCA阳性;CD21、CD35、CD1a等均阴性。结论指突状树突细胞肉瘤极为罕见,容易漏诊和误诊,熟悉其临床病理特点,依靠免疫组化和电镜可确诊。
Objective To investigate the diagnostic criteria and differential diagnosis of dendritic cell sarcoma in the extra-ocular process. Methods One case of dendritic cell sarcoma outside the finger was histopathologically and immunohistochemically stained and followed up. Results Tumor occurred in liver and spleen and died after 4 months of diagnosis. Microscopic examination: the tumor tissue was striated, spiral or messy arrangement, tumor cells oval, fusiform, less cytoplasm, nuclear oval or short fusiform, less chromatin, part of the nucleolus, mitosis and more see. Tumor cells S-100, CD68, Vimentin and LCA positive; CD21, CD35, CD1a, etc. were negative. Conclusions: Dendritic cell sarcoma is extremely rare, easily missed and misdiagnosed, familiar with its clinical and pathological features, and can be diagnosed by immunohistochemistry and electron microscopy.