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肾小管性酸中毒(Renal TubularAcidosis简称RTA)是一种较少见的综合征,特点是早期肾小球功能正常,而由于肾小管功能障碍引起代谢性酸中毒。Lighth-ood氏于1935年首次报道。我国自1958年董氏报道以来已逐渐受到重视。此综合征临床表现复杂,误诊极为普遍,给患者造成痛苦甚至死亡。如能及时诊治,又多具可治性。为此作者将本院73年以来收治的7例病例作一分析,并收集1858年至1983年9月间国内报道病例,共199例作一文献复习,重点讨论避免误诊问题。
Renal Tubular Acidosis (RTA) is a rare syndrome characterized by normal early glomerular function and metabolic acidosis due to renal tubular dysfunction. Lighthodo first reported in 1935. Since 1958, Dong’s report has been taken seriously in our country. The complex clinical manifestations, misdiagnosis is extremely common, causing pain and even death to patients. If timely diagnosis and treatment, but also more governance. For this reason, the author analyzed 7 cases admitted to our hospital for 73 years and collected domestic reported cases from 1858 to September 1983. A total of 199 cases were reviewed with a review of the literature, focusing on avoiding misdiagnosis.