新生儿先天性鱼鳞癣样红皮病在临床上实属少见。我院一产妇于1992—07—20分娩一男婴。现报告如下。寇某,21岁,农民,孕39周。孕期顺利,否认农药接触史、服药史,否认近亲结婚及家庭三代患此病史,即往健康,自然分娩。出生后,新生儿 Apgar 评分,1分钟评分8分,5分钟评分9分。体格检查:呼吸28次/分,心率132次/分,体重2150g,身长46cm,头围29cm,胸围30cm,前囱3cm×2cm。哭声宏亮,面容呆,颜面及全身皮肤淡红色,皮肤紧缩、硬、弹性差,口周可见破裂,眼睑外翻,结膜充血,轻度鼻塞,耳廓增厚,指、趾发黄、硬。检查阴茎正常,睾丸未降入阴囊。心肺正常,肝脾正常,各种 Newborn congenital ichthyosis erythematosis is clinically rare. A woman in our hospital gave birth to a baby boy on July 20, 1992. The report is as follows. Kou Mou, 21 years old, farmer, 39 weeks pregnant. Pregnancy smooth, deny the history of pesticide exposure, medication history, deny marriage and family history of three generations of this history, that is healthy, natural childbirth. After birth, neonatal Apgar score, 1 minute rating 8 points, 5 minutes rating 9 points. Physical examination: breathing 28 beats / min, heart rate 132 beats / min, weight 2150g, length 46cm, head circumference 29cm, chest circumference 30cm, before the chimney 3cm × 2cm. Clarity, face dignity, face and body skin pink, tight skin, hard, flexible, perioral rupture, eyelid valgus, conjunctival hyperemia, mild nasal obstruction, auricle thickening, finger toe yellow, hard. Check the penis normal, testicular did not fall into the scrotum. Normal heart and lung, liver and spleen normal, all kinds