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目的 :研究原发性骶骨肿瘤的临床特征 ,诊断 ,治疗方法及随访结果。方法 :复习文献 ,分析 12例原发性骶骨肿瘤的患者 ,其中脊索瘤 8例 ,骨巨细胞瘤 3例 ,骨肉瘤 1例。均行肿瘤切除 ,术后放疗或化疗 ,随访 5~ 7年。结果 :1例脊索瘤及 2例骨巨细胞瘤患者术后局部复发 ,再次手术切除 ,其他患者经随访术后局部及全身未见复发。结论 :脊索瘤在原发性骶骨肿瘤中的发病率居首 ,患者条件允许的前提下 ,原发性骶骨肿瘤的治疗应采取以手术为主的综合治疗。
Objective: To study the clinical features, diagnosis, treatment and follow-up of primary sacral tumors. Methods: We reviewed the literature and analyzed 12 patients with primary sacral tumors, including 8 chordoma, 3 giant cell tumor of bone and 1 osteosarcoma. Tumor resection, postoperative radiotherapy or chemotherapy, followed up for 5 to 7 years. Results: One case of chordoma and two cases of giant cell tumor of bone had local recurrence after operation. The patients were surgically resected. No other patients had local or systemic recurrence after follow-up. Conclusion: The incidence of chordoma in primary sacral tumors is the highest. Under the premise of patients’ condition, the treatment of primary sacral tumors should be based on the comprehensive surgical treatment.