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报告1例脂溢性类天疱疮.患者男,22岁.头面部红斑、水疱,伴剧烈瘙痒9个月.皮疹渐增大、增多,累及耳郭、胸部、背部,部分水疱破溃,形成糜烂面.皮损组织病理检查示局部表皮坏死,可见表皮下水疱,真皮血管周围淋巴细胞、嗜酸性粒细胞及中性粒细胞浸润.直接免疫荧光:基膜带IgG、C3呈带状沉积.用ELISA法检测大疱性类天疱疮(BP) 180抗体84 kU/L(正常值≤9 kU/L).结合临床、组织病理及血清学检查结果诊断为脂溢性类天疱疮.“,”A case of seborrheic pemphigoid is reported.A 22-year-old man presented with 9-month-history of erythematous,pruritic macules and patches on his scalp and cheeks topped with clear fluid-filled vesicles and bullae.The lesions gradually increased in number and spread to the pre-and post-auricular,chest and back with several erythematous erosions.Histopathological examination showed subepidermal blisters with perivascular infiltration of lymphocytes,eosinophils and neu trophils.Direct immunofluorescence showed linear deposition of IgG and C3 in the basement membrane zone.Serum enzymelinked immunosorbent assay of BP180 was positive(84 kU/L).According to the clinical and histopathologic features,and serological findings,the patient was diagnosed as seborrheic pemphigoid.