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作者从多年来所积累的临床及尸检材料中选择了12例此较特殊的再生障碍性贫血病例,讨论了本病和白血病的关系。材料共分为两组: 第一组共五例:临床诊断为亚急性不白血性网状细胞增生症或原血细胞增生症病理解剖检查最后诊断为再生障碍性贫血。本组患者的临床表现为皮肤苍内,有较轻的出血现象,无肝、脾及淋巴结肿大,有严重造血障碍,末梢血液中的三种有形成分均减少,并有多少不等(高达54—80%)的原血细胞出现。部分骨髓穿刺显示未分化细胞数增加(31—56.2%)。尸检结果:肝、脾及淋巴结均不肿大,脾脏和淋巴结的淋巴组织萎缩,股骨均呈脂肪化,部分病例于胸
The authors selected 12 cases of this particular type of aplastic anemia from clinical and autopsy materials accumulated over the years and discussed the relationship between this disease and leukemia. Materials were divided into two groups: the first group of five cases: the clinical diagnosis of subacute neutropenic or hematopoietic pathology anatomy of the final diagnosis of aplastic anemia. The clinical manifestations of this group of patients with skin Cang, a lighter bleeding, no liver, spleen and lymph nodes, severe hematopoietic disorders, peripheral blood of the three visible components are reduced, and how many different ( Up to 54-80%) of the original blood cells appear. Some bone marrow biopsy showed an increase of undifferentiated cells (31-56.2%). Autopsy results: Liver, spleen and lymph nodes are not enlarged, lymphoid tissue of the spleen and lymph node atrophy, femur showed fatty, some cases in the chest