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嗜铬细胞瘤是起源于肾上腺髓质、交感神经节或者其他部位的嗜铬组织的良性肿瘤,这种肿瘤持续性或者间断性的释放大量儿茶酚胺,引起持续性或阵发性高血压和多个器官功能及代谢紊乱[1]。其中肾上腺外嗜铬细胞瘤称为副神经节瘤,主要位于腹部肾上腺外的其他脏器,极少位于胸部。另外,肾上腺外肿瘤可以是多中心的,局部复发比例较高。下面就1例纵隔嗜铬细胞瘤的诊断与治疗进行较为详细的描述
Pheochromocytoma is a benign tumor of chromogranular tissue originating in the adrenal medulla, sympathetic ganglia, or other sites that releases large amounts of catecholamines, either persistently or intermittently, causing persistent or paroxysmal hypertension and multiple Organ dysfunction and metabolic disorders [1]. Of which extra-adrenal pheochromocytoma called paraganglioma, mainly in the abdominal organs other than the adventitia, rarely in the chest. In addition, extra-adrenal tumors can be multicentral, with a higher proportion of local recurrences. The following one case of mediastinal pheochromocytoma diagnosis and treatment are described in more detail