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患儿,女,生后10分钟,主因与其母血t型不合而入院,患儿为孕38周第八胎第五 产,其母妊娠前三胎流产,后四胎均因黄疸于 生后10~40天死亡。此次其母怀孕后抗体 效价为1:64~1:512。入院后查体:体重 3350g,足月儿貌,反应可,贫血貌,双下肢水 肿,心肺听诊未闻异常。肝肋下2cm,脾未触 及。四肢肌张力正常,新生儿反射存在。血 清学检查示:母为AB,CcDuee,子为A,ccDee,直接抗人球蛋白试验阳性,抗体释放t试验和游离抗体试验均为阳型。出生后脐血t总胆为75μmol/L,Hb120g/L。患儿生后12t小时出现皮肤黄染,并迅速加重。确诊为
Children, women, 10 minutes after birth, the main due to maternal blood t type admitted to the hospital for the 38th week of childbirth of the eighth child of the fifth birth, the third trimester abortion after the first trimester of pregnancy, the latter four were due to jaundice in Health After 10 to 40 days of death. The mother antibody titer after pregnancy for the 1: 64 ~ 1: 512. After admission, physical examination: weight 3350g, full-term appearance, the reaction can be, anemia appearance, both lower extremity edema, cardiopulmonary auscultation anomalies. Liver ribs 2cm, spleen not touched. Limb muscle tension is normal, neonatal reflex exists. Serological tests showed: the mother of AB, CcDuee, son of A, ccDee, direct anti-human globulin test positive, antibody release and free antibody test are positive. After birth, cord blood t total gall for 75μmol / L, Hb120g / L. Children born 12 t hours after the skin yellow dye, and rapidly aggravated. Diagnosed as