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原发性肠淋巴瘤仅占全都胃肠恶性肿瘤的1~2%,该病主要有两类:B 细胞(也包括免疫增殖性小肠病、恶性淋巴瘤息肉病和伯基特样淋巴瘤)和T细胞淋巴瘤。根据T 和B 淋巴细胞的抗原特征进行免疫表型分类是近年来的主要进展。Hall 等提出在免疫表型分类的基础上,再分为低度和高度恶性。他们强调B 细胞淋巴瘤多形性的重要性,并建议T 细胞瘤应保留形态学分类。
Primary intestinal lymphomas account for only 1 to 2% of all gastrointestinal malignancies. There are two main types of diseases: B cells (also known as immunoproliferative enteropathy, malignant lymphoma polyposis, and Burkitt-like lymphoma). And T-cell lymphoma. The classification of immune phenotypes based on the antigenic characteristics of T and B lymphocytes has been a major advance in recent years. Hall et al. proposed that on the basis of the immunophenotyping classification, it was subdivided into low-grade and highly malignant. They emphasized the importance of the polymorphism of B-cell lymphomas and suggested that T-cell tumors should retain morphological classification.