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目的:多房囊性肾瘤(multilocular cystic nephroma,MCN)临床极为罕见,国内外报道病例数少。本文报告2例并结合文献探讨MCN的概念及临床,病理学特征,影像学和治疗方案选择,旨在提高对MCN的诊治水平。方法:报告2例MCN患者临床资料,复习文献进行归纳分析。结果:1例患者行根治性肾切除术,1例患者行保留肾单位的肿瘤切除术,术后病理报告均为MCN。术后分别随访63个月,37个月均未见复发。结论:MCN是一种罕见肾脏良性肿瘤,其术前明确诊断困难,容易误诊,确诊依赖术后病理学诊断。首选手术治疗。
Objective: The clinical data of multilocular cystic nephroma (MCN) are extremely rare and few cases are reported at home and abroad. This article reports 2 cases combined with literature to explore the concept of MCN and clinical and pathological features, imaging and treatment options to improve the diagnosis and treatment of MCN level. Methods: The clinical data of 2 cases of MCN were reported and the literature reviewed. Results: One patient underwent radical nephrectomy and one patient underwent nephron excision. The pathological reports were all MCN. The patients were followed up for 63 months and 37 months respectively. Conclusion: MCN is a rare benign renal neoplasm. It is difficult to diagnose preoperatively and is easily misdiagnosed. Diagnosis depends on postoperative pathological diagnosis. Preferred surgical treatment.